Ovarian dysgenesis profoundly impacts fertility due to the absence or dysfunction of ovarian tissue, which is necessary for egg production. As a result, individuals with this condition are often infertile. However, advances in reproductive medicine provide options for family building. Egg donation and assisted reproductive technologies allow individuals with ovarian dysgenesis to conceive and carry a pregnancy if they have a functional uterus. Genetic counseling can help individuals understand their options and the implications of their genetic condition.